Good Prognosis of ALCAPA (Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery Syndrome) with Early Diagnosis and Surgical Treatment

Abstract

Introduction: ALCAPA Anomalous origin of the left main coronary artery (LCA) from the pulmonary artery (PA) is a rare malformation that presents with myocardial ischemia or infarction and/or cardiac failure in infants (1). Surgical correction to re-establish a two-coronary artery perfusion system is the treatment of choice (2). Objective: To present a case of ALCAPA with early diagnosis and treatment, and a very good prognosis. Case Relate: 6 months old girl admitted with symptoms of heart failure, Echo, ECG and Cath showed signs of ALCAPA with sever dilated cardiomyopathy. The baby sent for surgical repair, and direct implantation of the LCA into the ascending aorta was done successfully. The baby followed in our cardiology clinic monthly. After 6 month of surgical repair, the baby was good without any complain, all symptoms resolved, the Echo showed acceptable contractility and function, the dilated cardiomyopathy improved dramatically. Conclusion: In infants with DCM due to coronary artery anomalies, early diagnosis and surgical treatment with optimal timing provide an excellent prognosis.